Autor(es):
Robalo-Cordeiro, C. ; Morais, A.
Data: 2021
Identificador Persistente: https://hdl.handle.net/10316/100790
Origem: Estudo Geral - Universidade de Coimbra
Assunto(s): Awareness; Consensus; Diagnosis; Guidelines; Idiopathic pulmonary fibrosis; Adult; Awareness; Biopsy; Consensus; Cross-Sectional Studies; Female; Follow-Up Studies; Guideline Adherence; Humans; Idiopathic Pulmonary Fibrosis; Interdisciplinary Communication; Lung; Male; Middle Aged; Pathologists; Portugal; Practice Guidelines as Topic; Pulmonologists; Radiologists
Descrição
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive fibrotic interstitial lung disease of unknown cause, which predominantly manifests in older males. IPF diagnosis is a complex, multi-step process and delay in diagnosis cause a negative impact on patient survival. Additionally, a multidisciplinary team of pulmonologists, radiologists and pathologists is necessary for an accurate IPF diagnosis. The present study aims to assess how diagnosis and treatment of IPF are followed in Portugal, as well as the knowledge and implementation of therapeutic guidelines adopted by the Portuguese Society of Pulmonology.