Autor(es): Alves, Ana Sofia ; Antunes, Natalie ; Santos, Joana ; Reis, João Eurico ; Calvinho, Paulo
Data: 2022
Origem: Portuguese Journal of Cardiac Thoracic and Vascular Surgery
Assunto(s): Solitary Fibrous Tumor; Pleura; Hypoglycemia; Doege-Potter syndrome
Introduction: Solitary fibrous tumor of the pleura (SFTP) is a rare neoplasm that accounts for less than 5% of all pleural tumors. We present the case of a 73-year-old man with a history of recurrent episodes of severe hypoglycemia secondary to a large malignant SFTP. This paraneoplastic manifestation of SFTP occurs in less than 5% of cases and is referred to as Doege-Potter syndrome. Although rare, this is an important and reversible cause of hypoglycemia, which is resolved by complete surgical resection of the tumor. We describe the pathogenesis, diagnosis, and treatment of Doege-Potter syndrome. Key imaging findings and pathologic correlation are shown.
