Autor(es):
Pereira-da-Silva, T ; Galrinho, A ; Ribeiro, A ; Jalles, N ; Martelo, F ; Fragata, J ; Cruz Ferreira, R
Data: 2013
Identificador Persistente: http://hdl.handle.net/10400.17/1185
Origem: Repositório do Centro Hospitalar de Lisboa Central, EPE
Assunto(s): Mediastinite; HSM CAR; HSM CCT; HSJ ANPAT; Mediastino; Esclerose; Diagnóstico Diferencial; Ressonância Magnética; Neoplasias Cardíacas
Descrição
We report a case of a woman, aged 53 years, presenting with a right atrial mass due to idiopathic fibrosing mediastinitis with periaortic involvement. This challenging diagnosis was confirmed by different imaging modalities and histopathologic analysis. The diagnosis of cardiac tumours is often difficult. To our knowledge, this is the first reported case of an intracavitary cardiac mass due to fibrosing mediastinitis. This rare disorder, which is characterized by invasive proliferation of fibrous tissue within the mediastinum, should be included in the differential diagnosis of intracardiac tumours.