Coexistence of Pheochromocytoma and Renal Artery Stenosis in a Pediatric Patient with Hypertension

• Author(s): Serras, I ; Baeta Baptista, R ; Francisco, T ; Casimiro, A ; Lito, D ; Alves, R ; Abranches, M
• Date: 2018
• Persistent ID: http://hdl.handle.net/10400.17/3132
• Origin: Repositório do Centro Hospitalar de Lisboa Central, EPE
• Subject(s): Hypertension; Pheochromocytoma; Encephalopathy Syndrome; Renal Artery Stenosis; Child; HDE PED; HDE NEF PED; HDE CIR PED; HDE UCI PED
• Document Type: Journal article
• Language: English
• Contributor(s): Repositório da Unidade Local de Saúde São José

Description

Pheochromocytoma and renal artery stenosis are surgically treatable causes of hypertension. Although rare, the coexistence of pheochromocytoma and renal artery stenosis has been described in case reports. Common pathophysiological mechanisms other than extrinsic compression may be involved in this association, such as catecholamine-induced vasospasm. The early recognition of the association of pheochromocytoma with renal artery stenosis is essential for appropriate treatment planning. We present the case of a previously healthy tenyear- old boy who presented with hypertensive encephalopathy, tachycardia and diaphoresis. Hypertension was found to be secondary to a catecholamine-producing tumor associated with coexisting renal artery stenosis. Hypertension resolved a few months after successful pheochromocytoma excision, without renal artery revascularization.