Weaning Practices in Phenylketonuria Vary Between Health Professionals in Europe

• Autor(es): Pinto, A ; Adams, S ; Ahring, K ; Allen, H ; Almeida, MF ; Garcia-Arenas, D ; Arslan, N ; Assoun, M ; Atik Altınok, Y ; Barrio-Carreras, D ; Belanger Quintana, A ; Bernabei, SM ; Bontemps, C ; Boyle, F ; Bruni, G ; Bueno-Delgado, M ; Caine, G ; Carvalho, R ; Chrobot, A ; Chyż, K ; Cochrane, B ; Correia, C ; Corthouts, K ; Daly, A ; De Leo, S ; Desloovere, A ; De Meyer, A ; De Theux, A ; Didycz, B ; Dijsselhof, ME ; Dokoupil, K ; Drabik, J ; Dunlop, C ; Eberle-Pelloth, W ; Eftring, K ; Ekengren, J ; Errekalde, I ; Evans, S ; Foucart, A ; Fokkema, L ; François, L ; French, M ; Forssell, E ; Gingell, C ; Gonçalves, C ; Gökmen Özel, H ; Grimsley, A ; Gugelmo, G ; Gyüre, E ; Heller, C ; Hensler, R ; Jardim, I ; Joost, C ; Jörg-Streller, M ; Jouault, C ; Jung, A ; Kanthe, M ; Koç, N ; Kok, I L ; Kozanoğlu, T ; Kumru, B ; Lang, F ; Lang, K ; Liegeois, I ; Liguori, A ; Lilje, R ; Ļubina, O ; Manta-Vogli, P ; Mayr, D ; Meneses, C ; Newby, C ; Meyer, U ; Mexia, S ; Nicol, C ; Och, U ; Olivas, SM ; Pedrón-Giner, C ; Pereira, R ; Plutowska-Hoffmann, K ; Purves, J ; Re Dionigi, A ; Reinson, K ; Robert, M ; Robertson, L ; Rocha, JC ; Rohde, C ; Rosenbaum-Fabian, S ; Rossi, A ; Ruiz, M ; Saligova, J ; Gutiérrez-Sánchez, A ; Schlune, A ; Schulpis, K ; Serrano-Nieto, J ; Skarpalezou, A ; Skeath, R ; Slabbert, A ; Straczek, K ; Giżewska, M ; Terry, A ; Thom, R ; Tooke, A ; Tuokkola, J ; van Dam, E ; van den Hurk, TAM ; van der Ploeg, E C ; Vande Kerckhove, K ; Van Driessche, M ; van Wegberg, AMJ ; van Wyk, K ; Vasconcelos, C ; Velez García, V ; Wildgoose, J ; Winkler, T ; Żółkowska, J ; Zuvadelli, J ; MacDonald, A
• Data: 2019
• Identificador Persistente: http://hdl.handle.net/10400.17/3245
• Origem: Repositório do Centro Hospitalar de Lisboa Central, EPE
• Assunto(s): Phe-free infant formula; Phenylalanine; Phenylketonuria; Weaning; Infant;; HDE PED
• Tipo de Documento: Artigo científico
• Idioma: Inglês
• Contribuidor(es): Repositório da Unidade Local de Saúde São José

Descrição

In phenylketonuria (PKU), weaning is considered more challenging when compared to feeding healthy infants. The primary aim of weaning is to gradually replace natural protein from breast milk or standard infant formula with solids containing equivalent phenylalanine (Phe). In addition, a Phe-free second stage L-amino acid supplement is usually recommended from around 6 months to replace Phe-free infant formula. Our aim was to assess different weaning approaches used by health professionals across Europe.