Detalhes do Documento

Retroperitoneal desmoid tumor during pregnancy - case report

Autor(es): Xavier,Marta ; Ferreira,Carla ; Furtado,Antónia ; Ramalho,Graça

Data: 2021

Origem: SciELO Portugal

Assunto(s): Desmoid; Pregnancy; Case report.


Descrição

Abstract Desmoid-type fibromatosis is a rare neoplastic tumor of fibroblastic proliferation that arises from muscle, fascia or aponeurotic complexes. Although usually benign, it is capable of significant local morbidity resulting from infiltration of surrounding structures. The etiology of desmoid-type fibromatosis is multifactorial since genetic, endocrine, and physical factors play an important role in its pathogenesis. Prognosis is mainly related to the anatomical site. We report a case of an intra-abdominal desmoid-type fibromatosis, arising from the retroperitoneum, diagnosed at 15 weeks of gestation and resected during pregnancy. This case demonstrates de diagnostic and management challenge posed by an abdominal mass during pregnancy.

Tipo de Documento Relatório
Idioma Inglês
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