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Dorfman-Chanarin Syndrome: A Rare Cause of Metabolic Associated Fatty Liver Dis...

Costa,Rita Quelhas da; Laranjeira,Francisco; Ribeiro,Isaura Duarte; Santos,António Filipe; Nery,Filipe

Abstract Metabolic associated fatty liver disease became the most common form of chronic liver disease, in the vast majority of the cases related to increased insulin resistance or metabolic dysregulation. Yet, other causes may be implied. We report the late diagnosis of Dorfman-Chanarin syndrome in a non-alcoholic steatohepatitis previously labeled cirrhotic middle-aged man, with consanguineous parents, compli...

Data: 2022   |   Origem: SciELO Portugal

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