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Corrigendum to “The effects of casein glycomacropeptide on general health statu...
Pinto, Alex; Daly, Anne; Newby, Camille; Robotham, Abigail; Heales, Simon; Eaton, Simon; Aitkenhead, Helen; Gilmour, Kimberly; Jackson, RichardPublisher Copyright: © 2025 The Author(s); The authors regret typing errors in the abstract where the p-values should be adiponectin (p = 0.049) and total antioxidant capacity (p = 0.028) and in table 2 (page 5), the energy intake for AA should read 1762 (1298–2321) rather than 1762 (1298–1677). The authors would like to apologise for any inconvenience caused.
Protein intake and prevalence of overweight in patients with phenylketonuria
Rodrigues, Catarina; Sousa Barbosa, Catarina; de Almeida, Manuela Ferreira; Bandeira, Anabela; Martins, Esmeralda; Rocha, Sara; Guimas, ArlindoFunding Information: This work was supported by an Individual Research Agreement between BioMarin Pharmaceutical Inc. and CINTESIS, R&D Unit (reference UIDB/4255/2020). The supporting source had no such involvement or restrictions regarding publication.Anita MacDonald received research funding and honoraria from Nutricia, Vitaflo International, and Merck Serono. She is a member of the Advisory Board entitled EL...
Protein Substitute Absorption
Daly, Anne; Pinto, Alex; Evans, Sharon; Geberhiwot, Tarekegn; Jackson, Richard; César Rocha, Júlio; Tang, Jonathan C.Y.; MacDonald, AnitaFunding Information: This research was funded by Birmingham Children Hospital Charity Grant and Nutricia Research Grant Nutricia Ltd., Trowbridge, UK. Publisher Copyright: © 2025 by the authors.; Background: The rate at which amino acids (AAs) are absorbed from casein glycomacropeptide (CGMP) when given as a protein substitute in phenylketonuria (PKU) is unknown. This three-way randomised, controlled, crossover...
Blood Phenylalanine Levels in Patients with Phenylketonuria from Europe between...
Pinto, Alex; Ahring, Kirsten; Almeida, Manuela Ferreira; Ashmore, Catherine; Bélanger-Quintana, Amaya; Burlina, Alberto; Coşkun, Turgay; Daly, AnnePublisher Copyright: © 2024 by the authors.; Background: In 2011, a European phenylketonuria (PKU) survey reported that the blood phenylalanine (Phe) levels were well controlled in early life but deteriorated with age. Other studies have shown similar results across the globe. Different target blood Phe levels have been used throughout the years, and, in 2017, the European PKU guidelines defined new targets for...
The effects of casein glycomacropeptide on general health status in children wi...
Pinto, Alex; Daly, Anne; Newby, Camille; Robotham, Abigail; Heales, Simon; Eaton, Simon; Aitkenhead, Helen; Gilmour, Kimberly; Jackson, RichardFunding Information: This study was sponsored by Vitaflo International Ltd.\u00AE, UK and Arla Foods Ingredients Group P/S. Publisher Copyright: © 2024; In PKU, it is suggested that casein glycomacropeptide based protein substitute (GMP) may have physiological advantage when satiety, oxidative stress, renal function and inflammation are considered. Its prebiotic properties may also help gastrointestinal (GI) to...
Longitudinal Dietary Intake Data in Patients with Phenylketonuria from Europe
Pinto, Alex; Ahring, Kirsten; Almeida, Manuela Ferreira; Ashmore, Catherine; Bélanger-Quintana, Amaya; Burlina, Alberto; Coşkun, Turgay; Daly, AnneFunding Information: A.P. received an educational grant from Cambrooke Therapeutics and Biomarin and grants from Vitaflo International, Nutricia, Merck Serono, Biomarin, Mevalia, Galen, PIAM, and Applied Pharma Research to attend scientific meetings. This project is also part of A.P.\u2019s PhD, which is funded by Vitaflo International. A.D. received research funding from Vitaflo International and financial sup...
Total Protein Intake in Patients with PKU
Gomes, Melanie; Almeida, Manuela Ferreira; Barbosa, Catarina Sousa; Gama, Maria Inês; Peres, Maria; Pinto, Élia; MacDonald, Anita; Rocha, Júlio CésarFunding Information: CINTESIS-UIDB/04255/2020 and UIDP/04255/2020, a program financially supported by Fundação para a Ciência e Tecnologia/Ministério da Ciência, Tecnologia e Ensino Superior, through national funds is acknowledged. Publisher Copyright: © 2023 by the authors.; In PKU, the protein requirements are contentious. In 2018, we evaluated the protein intake in patients with PKU. Ninety-nine early treate...
Natural Protein Intake in Children with Phenylketonuria
Pinto, Alex; Daly, Anne; Rocha, Júlio César; Ashmore, Catherine; Evans, Sharon; Ilgaz, Fatma; Hickson, Mary; MacDonald, AnitaFunding Information: A.P. received an educational grant from Cambrooke Therapeutics and grants from Vitaflo International, Nutricia, Merck Serono, Biomarin, Mevalia, Galen, and Applied Pharma Research to attend scientific meetings. This project is also part of A.P’s PhD, which is funded by Vitaflo International. A.D. received research funding from Vitaflo International and financial support from Nutricia, Meval...
Body Composition Evaluation and Clinical Markers of Cardiometabolic Risk in Pat...
Luengo-Pérez, Luis M.; Fernández-Bueso, Mercedes; Ambrojo, Ana; Guijarro, Marta; Ferreira, Ana Cristina; Pereira-da-Silva, Luís; Moreira-Rosário, AndréCardiovascular diseases are the main cause of mortality worldwide. Patients with phenylketonuria (PKU) may be at increased cardiovascular risk. This review provides an overview of clinical and metabolic cardiovascular risk factors, explores the connections between body composition (including fat mass and ectopic fat) and cardiovascular risk, and examines various methods for evaluating body composition. It parti...
Impact on Diet Quality and Burden of Care in Sapropterin Dihydrochloride Use in...
Gama, Maria Inês; Daly, Anne; Ashmore, Catherine; Evans, Sharon; Moreira-Rosário, André; Rocha, Júlio César; MacDonald, AnitaFunding Information: M.I.G. has received a Recordati Rare Disease Grant Ed. 2021–2022 from the Portuguese Society of Metabolic Diseases (SPDM) to develop this work in the worth of 3000€. Funding Information: M.I.G. has received travelling grants from Cambrooke Therapeutics and Nutricia to attend scientific meetings. A.D. received research funding from Vitaflo International, financial support from Nutricia, Meva...