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Thrombotic complications in patients with COVID-19 : pathophysiological mechani...

Gasecka, Aleksandra; Borovac, Josip A.; Guerreiro, Rui Azevedo; Giustozzi, Michela; Parker, William; Caldeira, Daniel; Chiva-Blanch, Gemma

Introduction: Emerging evidence points to an association between severe clinical presentation of COVID-19 and increased risk of thromboembolism. One-third of patients hospitalized due to severe COVID-19 develops macrovascular thrombotic complications, including venous thromboembolism, myocardial injury/infarction and stroke. Concurrently, the autopsy series indicate multiorgan damage pattern consistent with mic...


Predictors of Fabry disease in patients with hypertrophic cardiomyopathy: how t...

Azevedo, Olga; Marques, Nuno; Reis, Liliana; Cruz, Inês; Craveiro, Nuno; Antunes, Hugo; Lourenço, Carolina; Gomes, Renata; Guerreiro, Rui Azevedo

Fabry disease (FD) is a treatable cause of hypertrophic cardiomyopathy (HCM). We aimed to determine the independent predictors of FD and to define a clinically useful strategy to discriminate FD among HCM.


Screening for Fabry disease in patients with left ventricular noncompaction

Azevedo, Olga; Marques, Nuno; Craveiro, Nuno; Pereira, Ana Rita; Antunes, Hugo; Reis, Liliana; Guerreiro, Rui Azevedo; Miltenberger-Miltenyi, Gabriel

It is unclear whether left ventricular noncompaction (LVNC) is a distinct cardiomyopathy or a morphologic manifestation of different cardiomyopathies. We previously reported a case of LVNC in a Fabry disease (FD) patient, but it remains to be clarified whether LVNC is a cardiac manifestation of FD, a coincidental finding or an overdiagnosis, which has major therapeutic implications. This study aims to determine...


Quinze anos de ecografia intravascular coronária em intervenção coronária percu...

Guerreiro, Rui Azevedo; Fernandes, Renato; Teles, Rui Campante; Silva, Pedro Canas da; Pereira, Hélder; Ferreira, Rui Cruz; Costa, Marco; Seixo, Filipe

A ecografia intravascular coronária tem ganhado importância nos laboratórios de hemodinâmica pela evidência de impacto prognóstico positivo para os doentes. Este trabalho tem como objetivo caraterizar a utilização de ecografia intravascular em intervencões coronárias percutâneas em Portugal.


Screening for Fabry disease in patients with left ventricular noncompaction

Azevedo, Olga; Marques, Nuno; Craveiro, Nuno; Pereira, Ana Rita; Antunes, Hugo; Reis, Liliana; Guerreiro, Rui Azevedo; Pontes dos Santos, Rui

It is unclear whether left ventricular noncompaction (LVNC) is a distinct cardiomyopathy or a morphologic manifestation of different cardiomyopathies. We previously reported a case of LVNC in a Fabry disease (FD) patient, but it remains to be clarified whether LVNC is a cardiac manifestation of FD, a coincidental finding or an overdiagnosis, which has major therapeutic implications. This study aims to determine...


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