4 documents found, page 1 of 1
Conscious sedation with inhaled 50% nitrous oxide/oxygen premix in photodynamic...
Cabete,Joana; Campos,Sara; Lestre,SaraPhotodynamic therapy has been described as an effective therapeutic option in selected cases of anogenital lichen sclerosus that are refractory to first-line treatments. However, procedure-related pain is a limiting factor in patient adherence to treatment. The authors report the case of a 75-year-old woman with highly symptomatic vulvar lichen sclerosus, successfully treated with photodynamic therapy. An inhal...
Do you know this syndrome?
Santos,Guida; Lestre,Sara; João,AlexandrePOEMS syndrome is a unique clinical entity, the diagnosis of which is made when polyneuropathy and monoclonal gammopathy occur together, associated with other changes such as organomegaly, endocrinopathy, skin changes and papilledema. Cutaneous manifestations are heterogeneous, with diffuse cutaneous hyperpigmentation, hemangiomas and hypertrichosis occurring more frequently. We report the case of a 65- year-ol...
Blastic plasmacytoid dendritic cell neoplasm
Lencastre,André; Cabete,Joana; João,Alexandre; Farinha,Pedro; Ferreira,Gilda; Lestre,SaraBlastic plasmacytoid dendritic cell neoplasm is a rare and aggressive hematodermic neoplasia with frequent cutaneous involvement and leukemic dissemination. We report the case of a 76-year-old man with a 2 month history of violaceous nodules and a tumor with stony consistency, located on the head, and mandibular, cervical and supraclavicular lymphadenopathies. Multiple thoracic and abdominal adenopathies were i...
Birt-Hogg-Dubé syndrome
Lencastre,André; Ponte,Pedro; Apetato,Margarida; Nunes,Luis; Lestre,SaraA 45-year-old woman with a history of renal carcinoma was observed for facial, cervical and truncal flesh-colored papules. Relatives had similar skin findings and a brother had repeated episodes of pneumothorax. The computerized tomography scan revealed multiple cysts on both lungs. A skin biopsy revealed a perifollicular fibroma. The clinical diagnosis of Birt-Hogg-Dubé syndrome (BHDS) was corroborated by iden...