Pediatric cystic kidney diseases include a diversity of hereditary or non‐hereditary conditions, whose phenotypic presen‐ tation can vary from asymptomatic to end‐stage renal disease. We report a case of a male with a prenatal diagnosis of pyelectasis. Throughout the first two years of life, serial renal ultrasound showed regression of pyelectasis, but increased renal echogenicity, first identified at three mon...