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Heidenhain Variant of Creutzfeldt-Jakob Disease in Brazil: a case report

Mendonça,Laura Furtado Pessoa de; Saffi,Pedro Maia Nobre Rocha; Martini,Luciana Lilian Louzada; Farage,Luciano; Camargos,Einstein Francisco

<p>Creutzfeldt-Jakob disease (CJD) is a rare spongiform encephalopathy characterized by a rapid neurodegenerative progress, caused by a misfolded variant of the cellular prion protein (PrP) known as PrPSc. The clinical presentation of sCJD includes a wide range of neurological signs of cortical, subcortical, or cerebellar origin, either isolated or in various combinations. Due to this protean clinical presentat...

Data: 2020   |   Origem: Oasisbr

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