Introduction: Castleman Disease (CD) is a rare polyclonal lymphoproliferative disorder characterized by massive growth of lymphoid tissue. The most common sites of disease are the chest, abdomen, neck, and axilla. Excisional biopsy is mandatory for diagnosis, and complete surgical resection the gold-standard treatment in unicentric CD. Case report: A ten-year-old girl was observed at the Emergency Department wi...
Aim: Mucormycosis infections are highly lethal in immunosuppressed patients. The authors present a rare case of successful treatment of the condition. Case description: A 14-year-old male with acute lymphoblastic lymphoma in remission was diagnosed with pansinusitis, cerebral osteomyelitis, and encephalitis with an abscess caused by Rhizopus sp. Neurosurgical drainage, endoscopic sinus surgery, and left eye enu...
Introduction: Castleman Disease (CD) is a rare polyclonal lymphoproliferative disorder characterized by massive growth of lymphoid tissue. The most common sites of disease are the chest, abdomen, neck, and axilla. Excisional biopsy is mandatory for diagnosis, and complete surgical resection the gold-standard treatment in unicentric CD. Case report: A ten-year-old girl was observed at the Emergency Department wi...
Aim: Mucormycosis infections are highly lethal in immunosuppressed patients. The authors present a rare case of successful treatment of the condition. Case description: A 14-year-old male with acute lymphoblastic lymphoma in remission was diagnosed with pansinusitis, cerebral osteomyelitis, and encephalitis with an abscess caused by Rhizopus sp. Neurosurgical drainage, endoscopic sinus surgery, and left eye enu...
Apresenta-se o caso clínico de uma criança de 4 anos, sexo masculino com história de dor no membro inferior direito, claudicação da marcha e exame objectivo sem outras alterações. Oa exames imagiológicos mostraram uma lesão osteolítica desde o colo até ao terço distai da diáfise femural. O doente foi referenciado para a nossa Instituição com o diagnóstico provável de Sarcoma de Ewing versus linfoma, Com o objec...
Objectivos: O objectivo deste estudo foi o de avaliar a sobrevivência, frequência de recidivas e sequelas em crianças com Doença de Hodgkin tratadas neste serviço nos últimos vinte anos. Material e Métodos: Foi efectuado um estudo de coorte retrospectivo. Foram analisados os seguintes parâmetros: idade, sexo, data do diagnóstico, tiemoglobina (Hb) (g/dl): <10,5 e > 10,5, velocidade de sedimentação (VS): > 40 mm...
Objectivos: Os catéteres venosos centrais (CVC) podem ser utilizados em crianças que requerem acesso venoso prolongado, nomeadamenle naquelas com doença oncológica. O objectivo deste estudo foi avaliar as complicações que levaram à remoção dos catéteres e comparar os dois tipos de CVC utilizados (CVC com componente externo e CVC totalmente implantados) no Serviço de Pediatria do IPOFG do Porto. Material e Métod...
Burkitt's lymphoma (BL) is a highly aggressive B-cell neoplasm characterized by the translocation and deregulation of the c-myc gene on chromosome 8. Three distinct clinical forms of BL are recognized: endemic, sporadic, and human immunodeficiency-associated. BL is a rapidly growing neoplasm requiring immediate diagnosis and treatment.We described and analyzed our experience with Burkitt's lymphoma (BL) diagnos...