Abstract OHVIRA syndrome is a rare congenital female anomaly, characterized by the triad: uterus didelphys, unilaterally obstructed hemivagina and ipsilateral renal agenesis. The authors present a case of a 12-year-old girl with cyclic abdominal pain, scarce catamenia and intense dysmenorrhea refractory to NSAIDs. An abdominal and pelvic computized tomography was carried out which revealed renal agenesis, dupli...