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Perioperative management of a girl with hemophilia B undergoing dorsolumbar spi...

Martinho, Liliana; Perry da Câmara, Luisa; Batalha, Sara; Rodrigues, Joana; Carioca, Filipa; Marques, Joana

Hemophilia B is a coagulation disorder characterized by a deficiency of clotting factor IX. Women are often heterozygous carriers of the disease, however if their clotting factor levels are less than 60%, they may have an increased bleeding tendency. This is even higher if levels are under 40%. We present a case of a 14-year-old female, with mild hemophilia B (hemophilia B carrier with factor IX level < 40%) wh...


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