2 documents found, page 1 of 1
Bundle Approach to Reduce Bloodstream Infections in Neutropenic Hematologic
Martinez, Jose Manuel; Leite, Luís; França, Daniela; Capela, Rita; Viterbo, Luísa; Varajão, Natalina; Martins, Ângelo; Oliveira, IsabelIntroduction: The objective of the study was to reduce, by a bundle of interventions, the global bloodstream infections and catheterrelated bloodstream infections rates in neutropenic hematology patients with a long-term central venous catheter.Material and Methods: This was a non-randomized prospective study. It was conducted in a 20-bed hematology oncology unit (Portuguese Institute of Oncology, Porto, Portug...
ERYTHROPOIETIC PROTOPORPHYRIA – A Family Study and Report of a Novel Mutation i...
Morais, Paulo; Mota, Alberto; Baudrier, Teresa; Ferreira, Olga; Trigo, Filipe; Cerqueira, Rita; Palmeiro, Aida; Tavares, Purificação; Azevedo, FilomenaErythropoietic protoporphyria (EPP) is a rare inherited disorder of heme biosynthesis caused in most patients by a deficient activity of the enzyme ferrochelatase (FECH), with a consequent accumulation of protoporphyrin (PP) in various tissues. We report a 16-year-old male (index case) with EPP characterized by acute episodes of painful photosensitivity in the photoexposed areas since his early infancy, permane...