Introduction: Appendix neoplasms are rare and identified in about 1% of all appendectomies, with the most common etiologies being first of epithelial origin and second, neuroendocrine. Neuroendocrine tumors are derived from enterochromaffin cells, producing the granules Chromogranin A and Synaptophysin and are the second most common histological type of appendix neoplasm, often found incidentally after appendec...