26 documents found, page 1 of 3

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Decreased health-related quality of life in children and adolescents with autoi...

Bozzini,Ana Beatriz; Neder,Luciana; Silva,Clovis A.; Porta,Gilda

Abstract Objective: The objective of this study was to evaluate the health-related quality of life in children and adolescents with autoimmune hepatitis. Methods: A cross-sectional assessment with the Pediatric Quality of Life Inventory 4.0 (PedsQL 4.0) was completed for 80 patients with autoimmune hepatitis and 45 healthy controls. Demographic data, prednisone dose, disease remission state, disease severity, a...

Date: 2019   |   Origin: Oasisbr

Mortality in adolescents and young adults with chronic diseases during 16 years...

Ramos,Gabriel F.; Ribeiro,Vanessa P.; Mercadante,Mariana P.; Ribeiro,Maira P.; Delgado,Artur F.; Farhat,Sylvia C.L.; Leal,Marta M.; Marques,Heloisa H.

ABSTRACT Objectives: To evaluate mortality in adolescents and young adult patients with chronic diseases followed in a Latin American tertiary hospital. Methods: A cross-sectional retrospective study was performed in a tertiary/academic hospital in the state of São Paulo, Brazil. Death occurred in 529/2850 (18.5%) adolescents and young adult patients with chronic diseases, and 25/529 (4.7%) were excluded due to...

Date: 2019   |   Origin: Oasisbr

Pediatric chronic patients at outpatient clinics: a study in a Latin American U...

Alveno,Renata A.; Miranda,Caroline V.; Passone,Caroline G.; Waetge,Aurora R.; Hojo,Elza S.; Farhat,Sylvia C.L.; Odone-Filho,Vicente; Tannuri,Uenis

Abstract Objective: To describe the characteristics of children and adolescentes with chronic diseases of outpatient clinics at a tertiary university hospital. Methods: A cross-sectional study was performed with 16,237 patients with chronic diseases followed-up in one year. The data were collected through the electronic system, according to the number of physician appointments in 23 pediatric specialties. Patie...

Date: 2018   |   Origin: Oasisbr

Contraception for adolescents with chronic rheumatic diseases

Lourenço,Benito; Kozu,Katia T.; Leal,Gabriela N.; Silva,Marco F.; Fernandes,Elisabeth G.C.; França,Camila M.P.; Souza,Fernando H.C.; Silva,Clovis A.

ABSTRACT Contraception is an important issue and should be a matter of concern in every medical visit of adolescent and young patients with chronic rheumatic diseases. This narrative review discusses contraception methods in adolescents with juvenile systemic lupus erythematosus (JSLE), antiphospholipid syndrome (APS), juvenile idiopathic arthritis (JIA) and juvenile dermatomyositis (JDM). Barrier methods are s...

Date: 2017   |   Origin: Oasisbr

Latent tuberculosis infection screening in juvenile idiopathic arthritis patien...

Brunelli,Juliana Barbosa; Bonfiglioli,Karina Rossi; Silva,Clovis A.; Kozu,Katia Tomie; Goldenstein-Schainberg,Claudia; Bonfa,Eloisa; Aikawa,Nadia Emi

Abstract Objectives: To evaluate, in an endemic country, the long-term efficacy of latent tuberculosis infection (LTBI) screening and primary prophylaxis in patients with JIA receiving TNF blockers. Methods: This was a retrospective cohort that included JIA patients eligible to anti-TNF therapy. Patients were screened for LTBI prior to anti-TNF using tuberculin skin test (TST), chest X-ray and history of exposu...

Date: 2017   |   Origin: Oasisbr

Disseminated histoplamosis in adolescent mimicking granulomatosis with polyangi...

van Weelden,Marlon; Viola,Gabriela R.; Kozu,Katia T.; Aikawa,Nadia E.; Ivo,Claudia M.; Silva,Clovis A.

Date: 2017   |   Origin: Oasisbr

Esophageal abnormalities in juvenile localized scleroderma: is it associated wi...

Valões,Clarissa C.M.; Novak,Glaucia V.; Brunelli,Juliana B.; Kozu,Katia T.; Toma,Ricardo K.; Silva,Clovis A.

Abstract Objective: To assess esophageal involvement (EI) in juvenile localized scleroderma (JLS) population and the possible association between this gastrointestinal manifestation and demographic data, clinical features, laboratory exams, treatments and outcomes. Methods: For a period of 30 years, 5881 patients with rheumatic diseases were followed in our Pediatric Rheumatology Division. EI was defined by the...

Date: 2017   |   Origin: Oasisbr

Nephrotic syndrome as the first manifestation of juvenile systemic scleroderma

Couto,Saulo B.; Sallum,Adriana M.; Henriques,Luciana S.; Malheiros,Denise M.; Silva,Clovis A.; Vaisbich,Maria H.

Date: 2017   |   Origin: Oasisbr

What are the benefits of two-dimensional speckle tracking echocardiography for ...

Leal,Gabriela Nunes; Diniz,Maria de Fátima; Brunelli,Juliana; Lianza,Alessandro C.; Sallum,Adriana M. E.; Silva,Clovis A.

Date: 2016   |   Origin: Oasisbr

Piomiosite no lúpus eritematoso sistêmico juvenil

Blay,Gabriela; Ferriani,Mariana P.L.; Buscatti,Izabel M.; França,Camila M.P.; Campos,Lucia M.A.; Silva,Clovis A.

Resumo A piomiosite é uma infecção piogênica da musculatura esquelética, decorrente da disseminação hematogênica e geralmente acompanhada de formação de abscesso localizado. Esta infecção da musculatura é raramente descrita em adultos com lúpus eritematoso sistêmico (LES) e, até onde se sabe, ainda não o foi em pacientes com LES juvenil (LESJ). De nossos 289 pacientes com LESJ, uma apresentou piomiosite. Diagno...

Date: 2016   |   Origin: Oasisbr

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