6 documents found, page 1 of 1
Arrhythmic risk stratification in patients with left ventricular ring-like scar
Parisi, Vanda; Graziosi, Maddalena; Lopes, Luis R.; Luca, Antonio De; Pasquale, Ferdinando; Tini, Giacomo; Targetti, Mattia; Cueto, Maria R.Aims Left ventricular (LV) ring-like scar on cardiac magnetic resonance (CMR) has been linked to malignant arrhythmias in patients with non-ischaemic cardiomyopathy. This study aimed to perform a comprehensive evaluation of this phenotype and to identify risk factors for life-threatening arrhythmic events (LAEs), a composite of sudden cardiac death (SCD), aborted SCD, and sustained ventricular tachycardia. Meth...
Role of Cardiovascular Magnetic Resonance in the Clinical Evaluation of Left Ve...
Aguiar Rosa, Silvia; Thomas, Boban; Pieroni, Maurizio; Maurizi, Niccolò; Zampieri, Mattia; Cappelli, Francesco; Marchi, Alberto; Pradella, SilviaLeft ventricular hypertrophy (LVH) is a frequent imaging finding in the general population. In order to identify the precise etiology, a comprehensive diagnostic approach should be adopted, including the prevalence of each entity that may cause LVH, family history, clinical, electrocardiographic and imaging findings. By providing a detailed evaluation of the myocardium, cardiovascular magnetic resonance (CMR) h...
Prognostic value of reduced heart rate reserve during exercise in hypertrophic ...
Ciampi, Quirino; Olivotto, Iacopo; Peteiro, Jesus; D’Alfonso, Maria; Mori, Fabio; Tassetti, Luigi; Milazzo, Alessandra; Monserrat, LorenzoBackground: Sympathetic dysfunction can be evaluated by heart rate reserve (HRR) with exercise test. Objectives: To determine the value of HRR in predicting outcome of patients with hypertrophic cardiomyopathy (HCM). Methods: We enrolled 917 HCM patients (age = 49 +/- 15 years, 516 men) assessed with exercise stress echocardiography (ESE) in 11 centres. ESE modality was semi-supine bicycle in 51 patients (6%), ...
Stress Echo 2030: the novel ABCDE-(FGLPR) protocol to define the future of imaging
Picano, Eugenio; Ciampi, Quirino; Cortigiani, Lauro; Arruda-Olson, Adelaide M.; Borguezan-Daros, Clarissa; de Castro e Silva Pretto, José LuisWith stress echo (SE) 2020 study, a new standard of practice in stress imaging was developed and disseminated: the ABCDE protocol for functional testing within and beyond CAD. ABCDE protocol was the fruit of SE 2020, and is the seed of SE 2030, which is articulated in 12 projects: 1-SE in coronary artery disease (SECAD); 2-SE in diastolic heart failure (SEDIA); 3-SE in hypertrophic cardiomyopathy (SEHCA); 4-SE ...
Clinical features and natural history of PRKAG2 Variant Cardiac Glycogenosis
Lopez-Sainz, Angela; Dominguez, Fernando; Rocha Lopes, Luis; Pablo Ochoa, Juan; Barriales-Villa, Roberto; Climent, Vicente; Linschoten, MarijkeBACKGROUND PRKAG2 gene variants cause a syndrome characterized by cardiomyopathy, conduction disease, and ventricular pre-excitation. Only a small number of cases have been reported to date, and the natural history of the disease is poorly understood. OBJECTIVES The aim of this study was to describe phenotype and natural history of PRKAG2 variants in a large multicenter European cohort. METHODS Clinical, electr...
The Portuguese Registry of Hypertrophic Cardiomyopathy : overall results
Cardim, Nuno; Brito, Dulce; Lopes, Luís Rocha; Freitas, António; Araújo, Carla; Belo, Adriana; Gonçalves, Lino; Mimoso, Jorge; Olivotto, IacopoIntroduction: We report the results of the Portuguese Registry of Hypertrophic Cardiomyopathy, an initiative that reflects the current spectrum of cardiology centers throughout the territory of Portugal. Methods: A direct invitation to participate was sent to cardiology departments. Baseline and outcome data were collected. Results: A total of 29 centers participated and 1042 patients were recruited. Four cente...