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A case of pediatric paraparesis secondary to an idiopathic acute transverse myelitis

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Resumo:Introduction: Acute transverse myelitis (ATM) refers to a frequently idiopathic, segmental spinal cord inflammation. It is a rare condition, in particular in children, and not previously reported in a family retinitis pigmentosa (RP) clinical setting. Case Report: An 11-year-old previously healthy girl, with a family history of RP, presented with a subacute flaccid paraparesis, with bilateral, up to the fourth dorsal level, mixed sensory hypoesthesia and autonomic dysfunction. Brain and spinal cord magnetic resonance imaging (MRI) showed an extensive, T2-hyperintense, non-contrast enhancing lesion from the second to fifth dorsal levels. Cerebrospinal fluid (CSF) and lab studies were normal, as the ophthalmologic observation. Treated with high-dose corticosteroids and intensive physical therapy, a significant recovery could be seen. Conclusion: Early pharmacological and physical treatment is fundamental and may indeed change the prognosis of this disease ATM. The family history of RP, although probably incidental, brings nevertheless the issue of a possible etiological contribution, or pathologic common pathways.
Autores principais:Teixeira, Joana
Outros Autores:Carvalho, Susana; Martins, Sofia; Pontes, Teresa; Machado, Álvaro; Antunes, Henedina
Assunto:Transverse myelitis Retinitis pigmentosa Paraparesis Neurogenic urinary bladder
Ano:2014
País:Portugal
Tipo de documento:artigo
Tipo de acesso:acesso aberto
Instituição associada:Universidade do Minho
Idioma:português
Origem:RepositóriUM - Universidade do Minho

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