Publicação
Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic
| Resumo: | Introduction: Congenital heart diseases are the most common congenital malformation in Portugal. Fetus diagnosed in utero are referenced to and born in a tertiary care center. Newborns with suspected congenital heart disease missed in the pre-natal screening program and born outside of a referral center that present with clinical severity are transported by the Pediatric Inter-hospital Transport system. Our objective was to analyze the last seven years of inter-hospital transport of newborns with suspected Congenital Heart Disease of Portugal’s northern region and study those who escape the prenatal screening program. Materials and Methods: Newborns with suspected congenital heart disease, transported between April 1st 2011 and March 30th 2018, were identified from the Pediatric Inter-hospital Transport System’s records and individually reviewed in the National Health Service’s informatic system. Results: Were included 195 transports, corresponding to 144 patients. Congenital heart disease was excluded in 46 patients. Of these 144 patients, 87 were born outside of the reference center. Transposition of great arteries was the most common congenital heart disease transported (16/87; 18.4%) and aortic coarctation (14/87; 16.1%) the second. Prenatal diagnosis was present in nine of these patients (10.3%). Discussion: Transport number stability may translate the constant incidence of congenital heart diseases and/or reflect a non-improving prenatal diagnosis rate. Technical challenges in transposition of great arteries’ prenatal diagnosis may explain the higher number of transports. It is necessary to guarantee the prenatal diagnosis of congenital heart diseases by intervening locally. |
|---|---|
| Autores principais: | Carvalho, Catarina |
| Outros Autores: | Grilo, Marta; Baptista, Maria João |
| Assunto: | Case series |
| Ano: | 2020 |
| País: | Portugal |
| Tipo de documento: | artigo |
| Tipo de acesso: | acesso aberto |
| Instituição associada: | Sociedade Portuguesa de Pediatria |
| Idioma: | inglês |
| Origem: | Portuguese Journal of Pediatrics |
| _version_ | 1868077505711177728 |
|---|---|
| author | Carvalho, Catarina |
| author2 | Grilo, Marta Baptista, Maria João |
| author2_role | author author |
| author_facet | Carvalho, Catarina Grilo, Marta Baptista, Maria João |
| author_role | author |
| country_str | PT |
| creators_json_txt | [{\"Person.name\":\"Carvalho, Catarina\"},{\"Person.name\":\"Grilo, Marta\"},{\"Person.name\":\"Baptista, Maria João\"}] |
| datacite.creators.creator.creatorName.fl_str_mv | Carvalho, Catarina Grilo, Marta Baptista, Maria João |
| datacite.rights.fl_str_mv | http://purl.org/coar/access_right/c_abf2 |
| datacite.subjects.subject.fl_str_mv | Case series |
| datacite.titles.title.fl_str_mv | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic Recém-nascidos com Suspeita de Cardiopatia Congénita com Necessidade de Transporte Inter-hospitalar: Revisão Casuística de 7 Anos |
| dc.creator.none.fl_str_mv | Carvalho, Catarina Grilo, Marta Baptista, Maria João |
| dc.identifier.none.fl_str_mv | https://doi.org/10.25754/pjp.2020.17936 |
| dc.language.none.fl_str_mv | eng |
| dc.publisher.none.fl_str_mv | Sociedade Portuguesa de Pediatria |
| dc.rights.none.fl_str_mv | http://purl.org/coar/access_right/c_abf2 |
| dc.rights.rights.copyright.fl_str_mv | This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. |
| dc.subject.none.fl_str_mv | Case series |
| dc.title.fl_str_mv | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic Recém-nascidos com Suspeita de Cardiopatia Congénita com Necessidade de Transporte Inter-hospitalar: Revisão Casuística de 7 Anos |
| dc.type.none.fl_str_mv | http://purl.org/coar/resource_type/c_6501 |
| description | Introduction: Congenital heart diseases are the most common congenital malformation in Portugal. Fetus diagnosed in utero are referenced to and born in a tertiary care center. Newborns with suspected congenital heart disease missed in the pre-natal screening program and born outside of a referral center that present with clinical severity are transported by the Pediatric Inter-hospital Transport system. Our objective was to analyze the last seven years of inter-hospital transport of newborns with suspected Congenital Heart Disease of Portugal’s northern region and study those who escape the prenatal screening program. Materials and Methods: Newborns with suspected congenital heart disease, transported between April 1st 2011 and March 30th 2018, were identified from the Pediatric Inter-hospital Transport System’s records and individually reviewed in the National Health Service’s informatic system. Results: Were included 195 transports, corresponding to 144 patients. Congenital heart disease was excluded in 46 patients. Of these 144 patients, 87 were born outside of the reference center. Transposition of great arteries was the most common congenital heart disease transported (16/87; 18.4%) and aortic coarctation (14/87; 16.1%) the second. Prenatal diagnosis was present in nine of these patients (10.3%). Discussion: Transport number stability may translate the constant incidence of congenital heart diseases and/or reflect a non-improving prenatal diagnosis rate. Technical challenges in transposition of great arteries’ prenatal diagnosis may explain the higher number of transports. It is necessary to guarantee the prenatal diagnosis of congenital heart diseases by intervening locally. |
| dirty | 0 |
| eu_rights_str_mv | openAccess |
| format | article |
| id | app_0ac8cf2ea22da93d46f5cbca63a2fc3a |
| identifier.doi.fl_str_mv | https://doi.org/10.25754/pjp.2020.17936 |
| instacron_str | spp |
| institution | Sociedade Portuguesa de Pediatria |
| instname_str | Sociedade Portuguesa de Pediatria |
| language | eng |
| network_acronym_str | app |
| network_name_str | Portuguese Journal of Pediatrics |
| oai_identifier_str | oai:ojs.revistas.rcaap.pt:article/17936 |
| organization_str_mv | urn:organizationAcronym:spp |
| person_str_mv | Carvalho, Catarina Grilo, Marta Baptista, Maria João |
| publishDate | 2020 |
| publisher.none.fl_str_mv | Sociedade Portuguesa de Pediatria |
| reponame_str | Portuguese Journal of Pediatrics |
| repository_id_str | urn:repositoryAcronym:app |
| service_str_mv | urn:repositoryAcronym:app |
| spelling | Sociedade Portuguesa de PediatriaenIntroduction: Congenital heart diseases are the most common congenital malformation in Portugal. Fetus diagnosed in utero are referenced to and born in a tertiary care center. Newborns with suspected congenital heart disease missed in the pre-natal screening program and born outside of a referral center that present with clinical severity are transported by the Pediatric Inter-hospital Transport system. Our objective was to analyze the last seven years of inter-hospital transport of newborns with suspected Congenital Heart Disease of Portugal’s northern region and study those who escape the prenatal screening program. Materials and Methods: Newborns with suspected congenital heart disease, transported between April 1st 2011 and March 30th 2018, were identified from the Pediatric Inter-hospital Transport System’s records and individually reviewed in the National Health Service’s informatic system. Results: Were included 195 transports, corresponding to 144 patients. Congenital heart disease was excluded in 46 patients. Of these 144 patients, 87 were born outside of the reference center. Transposition of great arteries was the most common congenital heart disease transported (16/87; 18.4%) and aortic coarctation (14/87; 16.1%) the second. Prenatal diagnosis was present in nine of these patients (10.3%). Discussion: Transport number stability may translate the constant incidence of congenital heart diseases and/or reflect a non-improving prenatal diagnosis rate. Technical challenges in transposition of great arteries’ prenatal diagnosis may explain the higher number of transports. It is necessary to guarantee the prenatal diagnosis of congenital heart diseases by intervening locally.engenNewborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years CasuisticptRecém-nascidos com Suspeita de Cardiopatia Congénita com Necessidade de Transporte Inter-hospitalar: Revisão Casuística de 7 AnosTranslatedTitleCarvalho, CatarinaCarvalhoCatarinaDepartment of Pediatrics, Faculty of Medicine, University of Porto, Porto, PortugalGrilo, MartaGriloMartaPediatric Intensive Care Unit, Centro Materno-Pediátrico, Centro Hospitalar Universitário de São João, Porto, PortugalBaptista, Maria JoãoBaptistaMaria JoãoDepartment of Pediatric Cardiology, Centro Materno-Pediátrico, Centro Hospitalar Universitário São João, Porto, PortugalEISSN2184-4453IsPartOfPISSN2184-3333IsPartOf2020-04-16DOIhttps://doi.org/10.25754/pjp.2020.17936http://purl.org/coar/access_right/c_abf2open accessCase serieshttp://purl.org/coar/resource_type/c_6501journal articlehttp://creativecommons.org/licenses/by-nc-nd/4.0This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.2020-04-16fulltextapplication/pdfPortuguese Journal of Pediatrics512 |
| spellingShingle | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic Carvalho, Catarina Case series |
| status | SINGLETON |
| subject.fl_str_mv | Case series |
| title | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| title_full | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| title_fullStr | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| title_full_unstemmed | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| title_short | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| title_sort | Newborns with Suspected Congenital Heart Disease Demanding Emergency Transport: Seven Years Casuistic |
| topic | Case series |
| topic_facet | Case series |
| url | https://doi.org/10.25754/pjp.2020.17936 |
| visible | 1 |