Publicação
Gravidez na Síndrome de Marfan: dois casos clínicos
| Resumo: | Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics. |
|---|---|
| Autores principais: | Amaral,Patrícia Isidro |
| Outros Autores: | Campos,Ana; Patrício,Lino |
| Assunto: | Marfan Syndrome Pregnancy Aortic dilatation |
| Ano: | 2016 |
| País: | Portugal |
| Tipo de documento: | relatório |
| Tipo de acesso: | acesso aberto |
| Instituição associada: | Fundação para a Ciência e Tecnologia |
| Idioma: | português |
| Origem: | SciELO Portugal |
| _version_ | 1868441862121979904 |
|---|---|
| author | Amaral,Patrícia Isidro |
| author2 | Campos,Ana Patrício,Lino |
| author2_role | author author |
| author_facet | Amaral,Patrícia Isidro Campos,Ana Patrício,Lino |
| author_role | author |
| country_str | PT |
| creators_json_txt | [{\"Person.name\":\"Amaral,Patrícia Isidro\"},{\"Person.name\":\"Campos,Ana\"},{\"Person.name\":\"Patrício,Lino\"}] |
| datacite.creators.creator.creatorName.fl_str_mv | Amaral,Patrícia Isidro Campos,Ana Patrício,Lino |
| datacite.rights.fl_str_mv | http://purl.org/coar/access_right/c_abf2 |
| datacite.subjects.subject.fl_str_mv | Marfan Syndrome Pregnancy Aortic dilatation |
| datacite.titles.title.fl_str_mv | Gravidez na Síndrome de Marfan: dois casos clínicos |
| dc.creator.none.fl_str_mv | Amaral,Patrícia Isidro Campos,Ana Patrício,Lino |
| dc.format.none.fl_str_mv | text/html |
| dc.identifier.none.fl_str_mv | http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302016000100012 |
| dc.language.none.fl_str_mv | por |
| dc.publisher.none.fl_str_mv | Euromédice, Edições Médicas Lda. |
| dc.rights.none.fl_str_mv | http://purl.org/coar/access_right/c_abf2 |
| dc.source.none.fl_str_mv | Acta Obstétrica e Ginecológica Portuguesa v.10 n.1 2016 |
| dc.subject.none.fl_str_mv | Marfan Syndrome Pregnancy Aortic dilatation |
| dc.title.fl_str_mv | Gravidez na Síndrome de Marfan: dois casos clínicos |
| dc.type.none.fl_str_mv | http://purl.org/coar/resource_type/c_93fc |
| description | Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics. |
| dirty | 0 |
| eu_rights_str_mv | openAccess |
| format | report |
| id | scielopt_f7cd874dde94d5ecdc5baf2c09d9b8cb |
| identifier.url.fl_str_mv | http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302016000100012 |
| instacron_str | SciELO |
| institution | Fundação para a Ciência e Tecnologia |
| instname_str | Fundação para a Ciência e Tecnologia |
| language | por |
| network_acronym_str | scielopt |
| network_name_str | SciELO Portugal |
| oai_identifier_str | oai:scielo:S1646-58302016000100012 |
| organization_str_mv | urn:organizationAcronym:scielo |
| person_str_mv | Amaral,Patrícia Isidro Campos,Ana Patrício,Lino |
| publishDate | 2016 |
| publisher.none.fl_str_mv | Euromédice, Edições Médicas Lda. |
| reponame_str | SciELO Portugal |
| repository_id_str | urn:repositoryAcronym:scielopt |
| service_str_mv | urn:repositoryAcronym:scielopt |
| spelling | Gravidez na Síndrome de Marfan: dois casos clínicosAmaral,Patrícia IsidroCampos,AnaPatrício,LinoMarfan SyndromePregnancyAortic dilatationopen accesshttp://purl.org/coar/access_right/c_abf2http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302016000100012URLhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302016000100012URLHasVersion2016-03-01Marfan syndrome is a connective tissue disorder, autosomal dominant, which affects multiple organ systems, namely the cardiovascular, ocular and skeletal. Morbidity and mortality result primarily from aortic and cardiac complications including dilatation, dissection and rupture of the aorta. As a result, pregnancy in women with the Marfan syndrome has an increased risk. Main causes of complications are related with hemodynamic and hormonal modifications caused by pregnancy. The approach to pregnancy in patients with this syndrome is challenging and deserves special care. A multidisciplinary surveillance plan should be developed with support from cardiology, maternal fetal medicine, anesthesiology, genetics and pediatrics.Euromédice, Edições Médicas Lda.Acta Obstétrica e Ginecológica Portuguesa v.10 n.1 2016text/htmlporreporthttp://purl.org/coar/resource_type/c_93fcother research product |
| spellingShingle | Gravidez na Síndrome de Marfan: dois casos clínicos Amaral,Patrícia Isidro Marfan Syndrome Pregnancy Aortic dilatation |
| status | SINGLETON |
| subject.fl_str_mv | Marfan Syndrome Pregnancy Aortic dilatation |
| title | Gravidez na Síndrome de Marfan: dois casos clínicos |
| title_full | Gravidez na Síndrome de Marfan: dois casos clínicos |
| title_fullStr | Gravidez na Síndrome de Marfan: dois casos clínicos |
| title_full_unstemmed | Gravidez na Síndrome de Marfan: dois casos clínicos |
| title_short | Gravidez na Síndrome de Marfan: dois casos clínicos |
| title_sort | Gravidez na Síndrome de Marfan: dois casos clínicos |
| topic | Marfan Syndrome Pregnancy Aortic dilatation |
| topic_facet | Marfan Syndrome Pregnancy Aortic dilatation |
| url | http://scielo.pt/scielo.php?script=sci_arttext&pid=S1646-58302016000100012 |
| visible | 1 |