Publicação
Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I
| Resumo: | Chiari malformation type 1 is a frequent finding in patients with craniosynostosis. The performance of suboccipital decompression as a standard treatment has been progressively questioned. Two symptomatic patients presenting multiple suture craniosynostosis associated Chiari malformation type 1 underwent cranial vault expansion using spring-mediated distraction at an early age (at 2 and 6 weeks). A complete resolution of Chiari symptoms was observed postoperatively and the postoperative cervical spine magnetic resonance imaging showed adequate decompression of the craniocervical junction. Spring mediated distraction at an early age may be an efficient solution to address symptomatic multisutural craniosynostosis associated Chiari malformation type 1. |
|---|---|
| Autores principais: | Jesus, Ana Rita Patrocínio de |
| Assunto: | Malformação de Arnold-Chiari Craniossinostoses |
| Ano: | 2015 |
| País: | Portugal |
| Tipo de documento: | dissertação de mestrado |
| Tipo de acesso: | acesso restrito |
| Instituição associada: | Universidade de Lisboa |
| Idioma: | inglês |
| Origem: | Repositório da Universidade de Lisboa |
| _version_ | 1866810357674147840 |
|---|---|
| author | Jesus, Ana Rita Patrocínio de |
| author_facet | Jesus, Ana Rita Patrocínio de |
| author_role | author |
| contributor_name_str_mv | Miguéns, José Repositório Científico de Acesso Aberto da ULisboa |
| country_str | PT |
| creators_json_txt | [{\"Person.name\":\"Jesus, Ana Rita Patrocínio de\"}] |
| datacite.contributors.contributor.contributorName.fl_str_mv | Miguéns, José Repositório Científico de Acesso Aberto da ULisboa |
| datacite.creators.creator.creatorName.fl_str_mv | Jesus, Ana Rita Patrocínio de |
| datacite.date.Accepted.fl_str_mv | 2015-01-01T00:00:00Z |
| datacite.date.available.fl_str_mv | 2016-10-26T14:46:42Z |
| datacite.date.embargoed.fl_str_mv | 2016-10-26T14:46:42Z |
| datacite.rights.fl_str_mv | http://purl.org/coar/access_right/c_16ec |
| datacite.subjects.subject.fl_str_mv | Malformação de Arnold-Chiari Craniossinostoses |
| datacite.titles.title.fl_str_mv | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| dc.contributor.none.fl_str_mv | Miguéns, José Repositório Científico de Acesso Aberto da ULisboa |
| dc.creator.none.fl_str_mv | Jesus, Ana Rita Patrocínio de |
| dc.date.Accepted.fl_str_mv | 2015-01-01T00:00:00Z |
| dc.date.available.fl_str_mv | 2016-10-26T14:46:42Z |
| dc.date.embargoed.fl_str_mv | 2016-10-26T14:46:42Z |
| dc.format.none.fl_str_mv | application/pdf |
| dc.identifier.none.fl_str_mv | http://hdl.handle.net/10451/24907 |
| dc.language.none.fl_str_mv | eng |
| dc.rights.none.fl_str_mv | http://purl.org/coar/access_right/c_16ec |
| dc.subject.none.fl_str_mv | Malformação de Arnold-Chiari Craniossinostoses |
| dc.title.fl_str_mv | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| dc.type.none.fl_str_mv | http://purl.org/coar/resource_type/c_bdcc |
| description | Chiari malformation type 1 is a frequent finding in patients with craniosynostosis. The performance of suboccipital decompression as a standard treatment has been progressively questioned. Two symptomatic patients presenting multiple suture craniosynostosis associated Chiari malformation type 1 underwent cranial vault expansion using spring-mediated distraction at an early age (at 2 and 6 weeks). A complete resolution of Chiari symptoms was observed postoperatively and the postoperative cervical spine magnetic resonance imaging showed adequate decompression of the craniocervical junction. Spring mediated distraction at an early age may be an efficient solution to address symptomatic multisutural craniosynostosis associated Chiari malformation type 1. |
| dirty | 0 |
| eu_rights_str_mv | restrictedAccess |
| format | masterThesis |
| fulltext.url.fl_str_mv | https://repositorio.ulisboa.pt/bitstreams/f5ad406b-847e-4f39-b2ad-05d7cadeb9b8/download |
| id | ul_0ff4cff32dbdc0d2bf77bf22e37aeaf5 |
| identifier.url.fl_str_mv | http://hdl.handle.net/10451/24907 |
| instacron_str | ul |
| institution | Universidade de Lisboa |
| instname_str | Universidade de Lisboa |
| language | eng |
| network_acronym_str | ul |
| network_name_str | Repositório da Universidade de Lisboa |
| oai_identifier_str | oai:repositorio.ulisboa.pt:10451/24907 |
| organization_str_mv | urn:organizationAcronym:ul |
| person_str_mv | Jesus, Ana Rita Patrocínio de |
| publishDate | 2015 |
| reponame_str | Repositório da Universidade de Lisboa |
| repository_id_str | urn:repositoryAcronym:ul |
| service_str_mv | urn:repositoryAcronym:ul |
| spelling | engpt_PTChiari malformation type 1 is a frequent finding in patients with craniosynostosis. The performance of suboccipital decompression as a standard treatment has been progressively questioned. Two symptomatic patients presenting multiple suture craniosynostosis associated Chiari malformation type 1 underwent cranial vault expansion using spring-mediated distraction at an early age (at 2 and 6 weeks). A complete resolution of Chiari symptoms was observed postoperatively and the postoperative cervical spine magnetic resonance imaging showed adequate decompression of the craniocervical junction. Spring mediated distraction at an early age may be an efficient solution to address symptomatic multisutural craniosynostosis associated Chiari malformation type 1.application/pdfpt_PTSpring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type IJesus, Ana Rita Patrocínio deMiguéns, JoséHostingInstitutionOrganizationalRepositório Científico de Acesso Aberto da ULisboae-mailmailto:repositorio@reitoria.ulisboa.ptrepositorio@reitoria.ulisboa.ptURNurn:tid:2013594802016-10-26T14:46:42Z20152015-01-01T00:00:00ZHandlehttp://hdl.handle.net/10451/24907http://purl.org/coar/access_right/c_16ecrestricted accessMalformação de Arnold-ChiariCraniossinostoses448732 bytesliteraturehttp://purl.org/coar/resource_type/c_bdccmaster thesishttp://purl.org/coar/access_right/c_16ecapplication/pdffulltexthttps://repositorio.ulisboa.pt/bitstreams/f5ad406b-847e-4f39-b2ad-05d7cadeb9b8/download |
| spellingShingle | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I Jesus, Ana Rita Patrocínio de Malformação de Arnold-Chiari Craniossinostoses |
| status | SINGLETON |
| subject.fl_str_mv | Malformação de Arnold-Chiari Craniossinostoses |
| title | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| title_full | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| title_fullStr | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| title_full_unstemmed | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| title_short | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| title_sort | Spring mediated cranial vault expansion in infants : an alternative treatment for symptomatic multisutural craniosynostosis associated Chiari malformation type I |
| topic | Malformação de Arnold-Chiari Craniossinostoses |
| topic_facet | Malformação de Arnold-Chiari Craniossinostoses |
| url | http://hdl.handle.net/10451/24907 |
| visible | 1 |